Document title: Sindrome de Prune Belly
Journal: Revista do Colegio Brasileiro de Cirurgioes
Database: PERIÓDICA
System number: 000283422
ISSN: 0100-6991
Authors: 1

Institutions: 1Faculdade de Medicina de Sao Jose do Rio Preto, Departamento de Cirurgia Pediatrica, Sao Jose do Rio Preto, Sao Paulo. Brasil
Year:
Season: Nov-Dic
Volumen: 31
Number: 6
Pages: 400-401
Country: Brasil
Language: Portugués
Document type: Artículo
Approach: Caso clínico
English abstract Prune Belly Syndrome is a fetal uropathy of unknown etiology with incidence of 1/35000 to 1/50000 alive been born, characterized by a classical triad: abdominal musculature congenital deficiency, bilateral criptorquidia and urinary tract malformations. The authors present a case of this rare pathology associated with a patent urachus. After complementary exams confirmed urinary tract alterations (bilateral ureterohidronefrosis and vesicoureteral reflux degree 5, besides urinary infection), the surgical approach was vesicostomy to decrease urinary infections and sepsis. Definitve surgery should be accomplished around the 12th month of life. Nowadays, the child is asymptomatic , with follow-up every two months, with return consultation bimonthly
Disciplines: Medicina
Keyword: Cirugía,
Pediatría,
Síndrome de Prune-Belly,
Recién nacidos,
Técnicas quirúrgicas
Keyword: Medicine,
Pediatrics,
Surgery,
Prune-Belly syndrome,
Newborn,
Surgical techniques
Full text: Texto completo (Ver HTML)