Revista: | Revista do Colegio Brasileiro de Cirurgioes |
Base de datos: | PERIÓDICA |
Número de sistema: | 000283422 |
ISSN: | 0100-6991 |
Autores: | Teixeira, Roni Leonardo1 Petreca, Alexandre Garcia, Patricia Andrea Torres |
Instituciones: | 1Faculdade de Medicina de Sao Jose do Rio Preto, Departamento de Cirurgia Pediatrica, Sao Jose do Rio Preto, Sao Paulo. Brasil |
Año: | 2004 |
Periodo: | Nov-Dic |
Volumen: | 31 |
Número: | 6 |
Paginación: | 400-401 |
País: | Brasil |
Idioma: | Portugués |
Tipo de documento: | Artículo |
Enfoque: | Caso clínico |
Resumen en inglés | Prune Belly Syndrome is a fetal uropathy of unknown etiology with incidence of 1/35000 to 1/50000 alive been born, characterized by a classical triad: abdominal musculature congenital deficiency, bilateral criptorquidia and urinary tract malformations. The authors present a case of this rare pathology associated with a patent urachus. After complementary exams confirmed urinary tract alterations (bilateral ureterohidronefrosis and vesicoureteral reflux degree 5, besides urinary infection), the surgical approach was vesicostomy to decrease urinary infections and sepsis. Definitve surgery should be accomplished around the 12th month of life. Nowadays, the child is asymptomatic , with follow-up every two months, with return consultation bimonthly |
Disciplinas: | Medicina |
Palabras clave: | Cirugía, Pediatría, Síndrome de Prune-Belly, Recién nacidos, Técnicas quirúrgicas |
Keyword: | Medicine, Pediatrics, Surgery, Prune-Belly syndrome, Newborn, Surgical techniques |
Texto completo: | Texto completo (Ver HTML) |