The importance of central auditory evaluation in Friedreich's ataxia



Document title: The importance of central auditory evaluation in Friedreich's ataxia
Journal: Arquivos de neuro-psiquiatria
Database: PERIÓDICA
System number: 000418866
ISSN: 0004-282X
Authors: 1
2
1
1
1
1
3
Institutions: 1Universidade Tuiuti do Parana, Departamento de Otoneurologia, Curitiba, Parana. Brasil
2Universidade Federal do Parana, Hospital de Clinicas, Curitiba, Parana. Brasil
3Hospital Pequeno Principe, Departamento de Neurologia, Curitiba, Parana. Brasil
Year:
Season: Mar
Volumen: 76
Number: 3
Pages: 170-176
Country: Brasil
Language: Inglés
Document type: Estadística o encuesta
Approach: Analítico
English abstract Objective: To assess central auditory function in Friedreich's ataxia. Methods A cross-sectional, retrospective study was carried out. Thirty patients underwent the anamnesis, otorhinolaryngology examination, pure tone audiometry, acoustic immittance measures and brainstem auditory evoked potential (BAEP) assessments. Results The observed alterations were: 43.3% in the pure tone audiometry, bilateral in 36.7%; 56.6% in the BAEP test, bilateral in 50%; and 46.6% in the acoustic immittance test. There was a significant difference (p < 0.05) in the comparison between the tests performed. Conclusion In the audiological screening, there was a prevalence of the descending audiometric configuration at the frequency of 4kHz, and absence of the acoustic reflex at the same frequency. In the BAEP test, there was a prevalence of an increase of the latencies in waves I, III and V, and in the intervals of interpeaks I-III, I-V and III-V. In 13.3% of the patients, wave V was absent, and all waves were absent in 3.3% of patients
Portuguese abstract Objetiv: Avaliar a função auditiva central na ataxia de Friedreich (AFRD). Métodos Foi realizado um estudo retrospectivo de corte transversal. 30 pacientes realizaram anamnese, avaliações otorrinolaringológica, audiológica, imitanciométrica e do potencial evocado auditivo de tronco encefálico (PEATE). Resultados As alterações observadas foram: 43,3% no exame audiométrico sendo 36,7% dos casos, bilateralmente; 56,6% na avaliação do PEATE com 50% dos casos, bilateralmente e 46,6% no exame imitanciométrico. Houve diferença significativa (p < 0,05) na comparação entre os exames realizados. Conclusão No exame audiológico, ocorreu uma preponderância maior da configuração audiométrica descendente a partir da freqüência de 4kHz e ausência do reflexo acústico na mesma frequência. No exame do PEATE, houve prevalência do aumento das latências nas ondas I, III e V, e nos intervalos dos interpicos I-III, I-V e III-V. Em 13,3% dos casos, a onda V estava ausente, e em 3,3% dos casos, todas as ondas estavam ausentes
Disciplines: Medicina
Keyword: Neurología,
Otorrinolaringología,
Diagnóstico,
Ataxia espinocerebelar,
Trastornos auditivos,
Ataxia de Friedreich,
Potenciales evocados auditivos,
Marcha
Keyword: Neurology,
Otolaryngology,
Diagnosis,
Spinocerebellar ataxia,
Hearing disorders,
Friedreich ataxia,
Auditory evoked potentials,
Gait
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