| Journal: | Annals of hepatology |
| Database: | PERIÓDICA |
| System number: | 000407830 |
| ISSN: | 1665-2681 |
| Authors: | Li, Hui1 Ma, Zhi1 Xie, Ying1 Tian, Feng1 |
| Institutions: | 1China Medical University, Shengjing Hospital, Shenyang, Liaoning. China |
| Year: | 2017 |
| Season: | May-Jun |
| Volumen: | 16 |
| Number: | 3 |
| Pages: | 460-464 |
| Country: | México |
| Language: | Inglés |
| Document type: | Artículo |
| Approach: | Caso clínico |
| English abstract | The Abernethy malformation is a rare congenital malformation defined by the presence of an extrahepatic portosystemic shunt. Although most patients are asymptomatic, clinical encephalopathy is present in 15% of cases. We present a patient with type 2 Abernethy malformation, hyperammonemia, and encephalopathy. Shunt closure was performed successfully using interventional angiography; however, hyperammonemia recurred 3 months later. The diagnosis of Abernethy malformation can be made easily, but the ideal patient management strategy has not yet been established. This is the first reported patient with recurrence of hyperammonemia after interventional treatment; we discuss the therapeutic options for Abernethy malformation |
| Disciplines: | Medicina |
| Keyword: | Gastroenterología, Sistema cardiovascular, Malformaciones congénitas, Vena portal, Malformacion de Abernethy, Hiperamonemia |
| Keyword: | Medicine, Cardiovascular system, Gastroenterology, Congenital malformations, Portal vein, Abernethy malformation, Hyperammonemia |
| Full text: | Texto completo (Ver PDF) |
