Cutaneous amyloidosis associated with autoimmune hepatitis-primary biliary cirrhosis overlap syndrome



Document title: Cutaneous amyloidosis associated with autoimmune hepatitis-primary biliary cirrhosis overlap syndrome
Journal: Annals of hepatology
Database: PERIÓDICA
System number: 000411825
ISSN: 1665-2681
Authors: 1
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Institutions: 1Universidad Autónoma de Nuevo León, Hospital Universitario Dr. José Eleuterio González, Monterrey, Nuevo León. México
Year:
Season: May-Jun
Volumen: 14
Number: 3
Pages: 416-419
Country: México
Language: Inglés
Document type: Artículo
Approach: Caso clínico, descriptivo
English abstract Cutaneous amyloidosis is a rare disease characterized by the deposition of amyloid in the dermis. It can be primary or secondary, depending on associated diseases. It has been linked to various autoimmune diseases, including primary biliary cirrhosis. We present the case of a patient with an autoimmune hepatitis-primary biliary cirrhosis overlap syndrome with concomitant cutaneous amyloidosis, a very unusual association, and discuss similar cases and possible pathophysiological implications
Disciplines: Medicina
Keyword: Gastroenterología,
Inmunología,
Hepatitis autoinmune,
Amiloidosis cutánea,
Colestasis,
Prurito
Keyword: Medicine,
Gastroenterology,
Immunology,
Autoimmune hepatitis,
Cutaneous amyloidosis,
Cholestasis,
Pruritus
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