Cutaneous amyloidosis associated with autoimmune hepatitis-primary biliary cirrhosis overlap syndrome



Título del documento: Cutaneous amyloidosis associated with autoimmune hepatitis-primary biliary cirrhosis overlap syndrome
Revista: Annals of hepatology
Base de datos: PERIÓDICA
Número de sistema: 000411825
ISSN: 1665-2681
Autors: 1
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Institucions: 1Universidad Autónoma de Nuevo León, Hospital Universitario Dr. José Eleuterio González, Monterrey, Nuevo León. México
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Període: May-Jun
Volum: 14
Número: 3
Paginació: 416-419
País: México
Idioma: Inglés
Tipo de documento: Artículo
Enfoque: Caso clínico, descriptivo
Resumen en inglés Cutaneous amyloidosis is a rare disease characterized by the deposition of amyloid in the dermis. It can be primary or secondary, depending on associated diseases. It has been linked to various autoimmune diseases, including primary biliary cirrhosis. We present the case of a patient with an autoimmune hepatitis-primary biliary cirrhosis overlap syndrome with concomitant cutaneous amyloidosis, a very unusual association, and discuss similar cases and possible pathophysiological implications
Disciplines Medicina
Paraules clau: Gastroenterología,
Inmunología,
Hepatitis autoinmune,
Amiloidosis cutánea,
Colestasis,
Prurito
Keyword: Medicine,
Gastroenterology,
Immunology,
Autoimmune hepatitis,
Cutaneous amyloidosis,
Cholestasis,
Pruritus
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