| Revue: | Revista médica de Chile |
| Base de datos: | PERIÓDICA |
| Número de sistema: | 000339438 |
| ISSN: | 0034-9887 |
| Autores: | Enríquez, Andrés1 Baeza, Ricardo1 Gabrielli, Luigi1 Córdova, Samuel1 Castro, Pablo1 |
| Instituciones: | 1Pontificia Universidad Católica de Chile, Departamento de Enfermedades Cardiovasculares, Santiago de Chile. Chile |
| Año: | 2011 |
| Periodo: | Jul |
| Volumen: | 139 |
| Número: | 7 |
| Paginación: | 864-871 |
| País: | Chile |
| Idioma: | Español |
| Tipo de documento: | Estadística o encuesta |
| Enfoque: | Descriptivo |
| Resumen en inglés | Non compaction cardiomyopathy is a rare disorder caused by the arrest of myocardial compaction during embryogenesis, leading to a non compacted endocardial layer with marked hypertrabeculation and deep recesses. Aim: To report the clinical and echocardiographic characteristics of a series of 15 adult patients with non-compaction cardiomyopathy. Patients and Methods: We included a total of 15 patients aged 52 ± 17 years (40% males) diagnosed at our echocardiography laboratory between January 2001 and July 2010. Results: Theform of presentation was heart failure in 53% of subjects, syncope in 20%o, ventricular arrhythmias in 13%o and stroke in 7%>. Left ventricular end-diastolic diameter was 66 ±11 mm and estimated ejection fraction was 27 ± 10%>. Apical and/or mid-ventricular segments of the left ventricle were involved in all the cases. Pulmonary hypertension was present in 40%o. The average follow-up was 19 months and no patient died during this period. Sixty seven percent ofthe patients had manifestations of heart failure, 27%o presented sustained ventricular arrhythmias and 20%> had atrial fibrillation orflutter, whereas 13%o had cerebral embolic events. An automated internal cardioverter defibrillator was implanted in 47%o of patients. Conclusions: Non-compaction cardiomyopathy is associated with high cardiovascular morbidity. The diagnosis is made in advanced stages of the disease, with significant dilation and ventricular dysfunction |
| Disciplinas: | Medicina |
| Palabras clave: | Diagnóstico, Sistema cardiovascular, Cardiomiopatías, Insuficiencia cardiaca, Evolución, Miocardiopatía no compactada, Criterios diagnósticos, Complicaciones |
| Keyword: | Medicine, Cardiovascular system, Diagnosis, Cardiomyopathies, Heart failure, Evolution, Non compaction cardiomyopathy, Diagnostic criteria, Complications |
| Texte intégral: | Texto completo (Ver HTML) |
