Ruptura atraumática del bazo como forma de presentación de la una amilosis AL en un paciente joven



Document title: Ruptura atraumática del bazo como forma de presentación de la una amilosis AL en un paciente joven
Journal: Revista médica de Chile
Database: PERIÓDICA
System number: 000454985
ISSN: 0034-9887
Authors: 1
2
2
3
4
5
6
Institutions: 1Centre Hospitalier de Creil, Service de Médecine Polyvalente, Creil., Oise. Francia
2Centre Hospitalier de Creil, Service de Chirurgie Digestive, Creil., Oise. Francia
3Centre Hospitalier de Creil, Service de Néphrologie, Creil., Oise. Francia
4Centre Hospitalier de Creil, Service d'Hématologie, Creil., Oise. Francia
5Centre Hospitalier de Creil, Service de Cardiologie, Creil., Oise. Francia
6Hôpitaux Universitaires de Strasbourg, Service de Médecine Interne, Diabète et Maladies Métaboliques, Strasbourg, Haut-Rhin. Francia
Year:
Season: May
Volumen: 150
Number: 5
Pages: 688-690
Country: Chile
Language: Español
Document type: Artículo
Approach: Caso clínico
English abstract We report a 35-year-old sportive man who was admitted to the emergency department for worsening of acute spontaneous abdominal pain appearing at rest. He only referred having lifted a tree trunk the day before, but he was used to perform such physical efforts. The clinical course at the emergency department was marked by the development of severe anemia secondary to a progressive splenic hematoma and acute pulmonary distress. The patient benefited from total splenectomy. Laboratory data showed hypogammaglobulinemia, proteinuria and the anatomopathological examinations of both spleen and kidneys were consistent with light chain amyloidosis
Disciplines: Medicina
Keyword: Metabolismo y nutrición,
Amiloidosis,
Proteinuria,
Ruptura esplénica
Keyword: Metabolism and nutrition,
Amyloidosis,
Proteinuria,
Splenic rupture
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