| Journal: | Revista da Associacao Medica Brasileira |
| Database: | PERIÓDICA |
| System number: | 000307406 |
| ISSN: | 0104-4230 |
| Authors: | Juang, J.M1 Silva, A.C.L.G Pires, M.C Valente, Y.S Sittart, J.A.S |
| Institutions: | 1Hospital do Servidor Publico Estadual de Sao Paulo, Servico de Dermatologia, Sao Paulo. Brasil |
| Year: | 1998 |
| Season: | Ene-Mar |
| Volumen: | 44 |
| Number: | 1 |
| Pages: | 50-52 |
| Country: | Brasil |
| Language: | Portugués |
| Document type: | Artículo |
| Approach: | Caso clínico, descriptivo |
| English abstract | The neurocutaneous melanosis is a rare syndrome in which the congenital melanocytic nevi and excessive melanosis are the main features. The syndrome seems to be a morphogenesis error of the embryonic neuroectoderm. A clinical case with necroscopy in a 19 year-old man who had developed malign melanoma in his central nervous system is reported |
| Portuguese abstract | A melanose neurocutânea é uma síndrome rara caracterizada por nevos melanocíticos congênitos gigantes e excessiva melanose da leptomeninge. A síndrome parece representar um erro na morfogênese do neuroectoderma embrionário. Os autores apresentam o caso e necropsia de um paciente masculino de 19 anos que desenvolveu melanoma maligno do sistema nervoso central |
| Disciplines: | Medicina |
| Keyword: | Dermatología, Neurología, Oncología, Melanosis neurocutánea, Melanoma, Sistema nervioso central, Nevus congénito |
| Keyword: | Medicine, Dermatology, Neurology, Oncology, Neurocutaneous melanosis, Melanoma, Central nervous system, Congenital naevus |
| Full text: | Texto completo (Ver HTML) |
