Granulomatose de Wegener e estenose subglótica: descrição de caso



Document title: Granulomatose de Wegener e estenose subglótica: descrição de caso
Journal: Revista brasileira de otorrinolaringologia
Database: PERIÓDICA
System number: 000306615
ISSN: 0034-7299
Authors: 1


Institutions: 1Hospital Universitario Evangelico de Curitiba, Curitiba, Parana. Brasil
Year:
Season: May-Jun
Volumen: 70
Number: 3
Pages: 419-422
Country: Brasil
Language: Portugués
Document type: Artículo
Approach: Caso clínico
English abstract We describe a patient with Wegener Granulomatosis being treated with steroids and cyclofosfamide that developed progressive dyspnea and hoarseness despite of treatment. Investigation showed a subglotic stenosis. The dyspnea was relieved by tracheotomy. We discuss the differential diagnosis as well as a number of treatment modalities in patients with Wegener granulomatosis and subglottic stenosis
Portuguese abstract Descreve-se o caso de um paciente com Granulomatose de Wegener, em tratamento com esteróides e ciclofosfamida, que, apesar do tratamento, evoluiu com dispnéia progressiva e rouquidão. A investigação mostrou tratar-se de uma estenose subglótica, sendo a dispnéia prontamente aliviada com a traqueostomia. São discutidos diagnósticos diferenciais e modalidades de tratamentos de estenose subglótica em portadores de Wegener
Disciplines: Medicina
Keyword: Otorrinolaringología,
Terapéutica y rehabilitación,
Diagnóstico diferencial,
Granulomatosis de Wegener,
Estenosis subglótica,
Vasculitis,
Anticuerpos anticitoplasma de neutrófilos
Keyword: Medicine,
Otolaryngology,
Therapeutics and rehabilitation,
Differential diagnosis,
Wegener granulomatosis,
Subglotic stenosis,
Vasculitis,
Neutrophil anticytoplasmic antibodies
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