Journal: | Jornal brasileiro de pneumologia |
Database: | PERIÓDICA |
System number: | 000297501 |
ISSN: | 1806-3713 |
Authors: | Barbas, Carmen Silvia Valente1 Borges, Eduardo da Rosa Antunes, Telma |
Institutions: | 1Universidade de Sao Paulo, Faculdade de Medicina, Sao Paulo. Brasil |
Year: | 2005 |
Season: | Jul |
Volumen: | 31 |
Pages: | 4-8 |
Country: | Brasil |
Language: | Portugués |
Document type: | Artículo |
Approach: | Caso clínico, descriptivo |
English abstract | The primary forms of pulmonary vasculitis are characterized by an inflammatory process in the pulmonary vessel walls, leading to pulmonary ischemia and hemorrhage and the consequent clinical and radiological manifestations. These forms of vasculitis are accompanied by symptoms involving the skin, peripheral nerves, kidneys, sinuses, eyes, ears and gastrointestinal tract, as well as the cardiac and central nervous systems. The diagnosis is made through analysis of the clinical, radiological and pathological data. When treatment with corticosteroids and immunosuppressive therapy is initiated early, remission rates are high |
Portuguese abstract | As vasculites pulmonares primárias são caracterizadas por processo inflamatório na parede dos vasos pulmonares que leva a isquemia e hemorragia pulmonar com as conseqüentes expressões clínicas e radiológicas. As vasculites pulmonares primárias são acompanhadas de expressão sistêmicas cutâneas, em nervos periféricos, rins, seios da face, olhos e ouvidos, além do trato gastrintestinal, e sistemas cardíaco e nervoso central. O diagnóstico é feito através da associação das informações clínicas, radiológicas e anatomopatológicas. O tratamento com corticosteróides e imunossupressores deve ser instituído precocemente e apresenta altas taxas de remissão |
Disciplines: | Medicina |
Keyword: | Diagnóstico, Neumología, Terapéutica y rehabilitación, Inmunosupresores, Lesiones cutáneas, Ojos, Vasculitis, Enfermedades pulmonares, Granulomatosis de Wegener, Síndrome de Churg-Strauss |
Keyword: | Medicine, Diagnosis, Pneumology, Therapeutics and rehabilitation, Immunosuppressive agents, Skin lesions, Eyes, Vasculitis, Pulmonary diseases, Wegener granulomatosis, Churg-Strauss syndrome |
Full text: | Texto completo (Ver HTML) |