Doenca pulmonar intersticial associada a bronquiolite respiratoria



Document title: Doenca pulmonar intersticial associada a bronquiolite respiratoria
Journal: Jornal brasileiro de pneumologia
Database: PERIÓDICA
System number: 000297392
ISSN: 1806-3713
Authors: 1



Institutions: 1Hospital do Servidor Publico Estadual, Sao Paulo. Brasil
Year:
Season: Nov-Dic
Volumen: 30
Number: 6
Pages: 574-580
Country: Brasil
Language: Portugués
Document type: Artículo
Approach: Caso clínico, descriptivo
English abstract Respiratory bronchiolitis-associated interstitial lung disease is one of many within the spectrum of smoking-related diffuse infiltrative lung diseases. The clinical and functional characteristics are typically subtle. Herein, we describe two cases of diagnosed through open-lung biopsy, and characterized by insidious evolution of dyspnea, digital clubbing, cystic lesions on computed tomography scans, and hipoxemia upon exertion. We emphasize that, when smokers are evaluated, it is imprtant to consider a diagnosis of respiratory bronchiolitis-associated interstitial lung disease in the context of interstitial cystitis, as well as in that of lymphangioleiomyomatosis, eosinophilic granuloma and idiophatic pulmonary fibrosis
Portuguese abstract A doença pulmonar intersticial associada a bronquiolite respiratória faz parte do espectro anatomopatológico das lesões pulmonares infiltrativas difusas induzidas pela fumaça de cigarro. Raramente tem apresentação clínico-funcional exuberante. Descrevemos dois casos diagnosticados por biópsia pulmonar aberta, caracterizados por dispnéia de evolução insidiosa, baqueteamento digital, lesões císticas à tomografia computadorizada e hipoxemia ao exercício. Enfatizamos considerar, em indivíduos tabagistas, a doença pulmonar intersticial associada a bronquiolite respiratória no contexto das pneumopatias intersticiais císticas, juntamente com a linfangioleiomiomatose, o granuloma eosinofílico e a fibrose pulmonar idiopática
Disciplines: Medicina
Keyword: Neumología,
Anatomía e histología,
Tabaquismo,
Enfermedades pulmonares,
Bronquiolitis,
Enfermedad intersticial pulmonar
Keyword: Medicine,
Pneumology,
Smoking,
Pulmonary diseases,
Bronchiolitis,
Interstitial lung disease,
Anatomy and histology
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