Ureteral calcinosis in juvenile dermatomyositis: successful precocious surgical management



Document title: Ureteral calcinosis in juvenile dermatomyositis: successful precocious surgical management
Journal: International braz j urol
Database: PERIÓDICA
System number: 000296882
ISSN: 1677-5538
Authors: 1

Institutions: 1Universidade de Sao Paulo, Escola de Medicina, Sao Paulo. Brasil
Year:
Season: Sep-Oct
Volumen: 32
Number: 5
Pages: 574-577
Country: Brasil
Language: Inglés
Document type: Artículo
Approach: Caso clínico, descriptivo
English abstract We report a successful surgical intervention to repair bilateral ureteral strictures in a child with juvenile dermatomyositis (JDM) and ureteral calcinosis. This is the fourth reported case in medical literature. A 9-year-old-girl with severe JDM, a rare connective tissue disease characterized by skin and muscles vasculitis, was under immunosuppressive therapy. In the course of the disease, she presented recurrent urinary tract infections. Bilateral ureteral dilation was detected by ultrasound (US) and intravenous pyelogram (IVP). CT scan showed bilateral ureteral calculus. Ureteroscopy revealed bilateral ureteral calcinosis, confirmed by histopathological analysis. Bilateral double-J stents were placed, resulting in transient improvement of ureteral dilation and infection, but only the surgical removal of abnormal ureteral portions was successful. In conclusion, endourological approach is recommended for diagnosis of urinary tract involvement by JDM because radiological evaluation can be misleading. The immunosuppressive treatment and the resection of damaged ureteral segments have allowed the control of urinary complications
Disciplines: Medicina
Keyword: Cirugía,
Dermatología,
Nefrología,
Ureteros,
Calcinosis,
Dermatomiositis,
Ureteroscopía
Keyword: Medicine,
Dermatology,
Nephrology,
Surgery,
Ureters,
Calcinosis,
Dermatomyositis,
Ureteroscopy
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