Leiomyosarcoma: an unusual cardiac tumor. Case report and literature review



Document title: Leiomyosarcoma: an unusual cardiac tumor. Case report and literature review
Journal: Cardiovascular and Metabolic Science (Ciudad de México)
Database: PERIÓDICA
System number: 000456044
ISSN: 2954-3835
Authors: 1
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Institutions: 1Hospital Civil de Guadalajara Fray Antonio Alcalde, Guadalajara, Jalisco. México
Year:
Volumen: 30
Number: 1
Pages: 34-37
Country: México
Language: Inglés
Document type: Artículo
Approach: Caso clínico
Spanish abstract Paciente femenino de 17 años, que comienza su padecimiento actual tres semanas previas, presentando disnea de medianos esfuerzos, progresando hasta presentar disnea en reposo y ortopnea, agregándose cinco días previos a su ingreso hemoptisis. Tres días antes presentó síncope, motivo por el cual es llevada al Servicio de Urgencias de otro hospital, donde diagnosticaron abdomen agudo secundario a colecistitis. Ingresó a colecistectomía, donde detectaron hepatomegalia, obteniendo biopsia. Se le indicó tomografía contrastada de tórax y abdomen donde detectan un tumor dependiente de la aurícula derecha con invasión de pericardio. Se realizó ecocardiograma transtorácico que demostró un tumor hiperecoico, que cubría la totalidad de la aurícula derecha, la cual protruía a través de la válvula tricúspide. Es trasladada a nuestro hospital y, secundario a insuficiencia cardiaca aguda, se le realizó cirugía, resecando 80% del tumor. Se confirmó por patología leiomiosarcoma de alto grado. La paciente fallece dos semanas después secundario a choque séptico refractario
English abstract A 17-year-old female was admitted to the hospital with progressive shortness of breath. It started three weeks before admission, and initially presented only on moderate exertion, worsening until it was present at rest and accompanied with orthopnea. Five days before admission, she developed hemoptysis. Three days before, she had a syncope and was taken to the emergency department of a nearby hospital. After she was examined, an acute abdominal pain secondary to cholecystitis was diagnosed. Cholecystectomy was performed and as an additional finding, surgeons reported hepatomegaly and took a liver biopsy. After these, an abdominal and chest computed tomography (CT scan) with IV contrast was performed, where a right atrial tumor with pericardial extension was reported. Based on this, they decided to perform a transthoracic echocardiogram and discovered a hyper-echogenic right atrial tumor, covering the entire cavity and protruding through the tricuspid valve. She was transferred to our hospital and taken to cardiac surgery due to worsening heart failure symptoms, where 80% of the tumor was resected. A high grade leiomyosarcoma was reported. A couple weeks later, the patient died secondary to refractory septic shock
Disciplines: Medicina
Keyword: Sistema cardiovascular,
Oncología,
Tumores cardiacos,
Leiomiosarcoma,
Aurícula derecha,
Manifestaciones clínicas
Keyword: Cardiovascular system,
Oncology,
Cardiac tumors,
Leiomyosarcoma,
Right atrium,
Clinical manifestations
Full text: https://www.medigraphic.com/pdfs/cardiovascuar/cms-2019/cms191e.pdf