Sindrome da medula presa. Registro de dois casos



Document title: Sindrome da medula presa. Registro de dois casos
Journal: Arquivos de neuro-psiquiatria
Database: PERIÓDICA
System number: 000077888
ISSN: 0004-282X
Authors: 1

Institutions: 1Fundacao Benjamin Guimaraes, Belo Horizonte, Minas Gerais. Brasil
Year:
Season: Jun
Volumen: 44
Number: 2
Pages: 179-184
Country: Brasil
Language: Portugués
Document type: Artículo
Approach: Caso clínico
English abstract The tethered spinal cord syndrome is a disease that ir part of the group of spinal dysraphisms, that was recently recognized as an individualized nosological entity, yet not frequently diagnosed among us. It is characterized by shortenning and thickening of the filum terminale which prevents the ascent of the spinal cord into spinal canal, the conus medularis abnormaly remainning in a low place. It is associated in all cases with spina bifida. The diagnosis is simple, once the disease is suspected. It is manifested by progressive motor or sensory deficit in the legs, urinary incontinence, scoliosis and leg or back pain, specially in young children. The plain lumbosacral RX always shows spina bifida. Myelography makes the diagnostic. It shows, basically, the negative image of the thickened filum terminale and the low placed conus medularis. Other exams which can help are the computadorized tomography and the ultra-sound of the spinal cord. The surgical treatment is very simple and heals without sequels if done in due time. It consists in a sectioning of the filum terminale through laminectomy Two cases diagnosed and treated at Hospital da Baleia, from Fundação Benjamim Guimarães, Belo Horizonte, are reported in this paper
Portuguese abstract Registro de dois casos da síndrome de medula presa nos quais o estabelecimento correto do diagnóstico permitiu adotar conduta terapêutica adequada. Esta consiste na ressecção cirúrgica do filum terminale. São comentados aspectos embriológicos e fisiopatogênicos de interesse à síndrome, bem como são analisadas suas manifestações clínicas principais, os exames complementares que possibilitam o diagnóstico, particularmente a mielografia, e aspectos da terapêutica cirúrgica
Disciplines: Medicina
Keyword: Cirugía,
Diagnóstico,
Neurología,
Pediatría,
Genética,
Médula espinal,
Malformaciones congénitas,
TAC,
Embriología,
Mielografía,
Niños
Keyword: Medicine,
Diagnosis,
Neurology,
Pediatrics,
Surgery,
Spinal cord,
Congenital malformations,
CAT,
Embryology,
Myelography,
Children,
Genetics
Full text: Texto completo (Ver PDF)