Journal: | Acta pediátrica de México |
Database: | PERIÓDICA |
System number: | 000328667 |
ISSN: | 0186-2391 |
Authors: | Lizárraga López, Sandra Luz1 Zárate Castañón, Patricia1 Bobadilla Aguirre, Alfredo1 Melgoza Arcos, Ma. Eugenia1 |
Institutions: | 1Instituto Nacional de Pediatría, Departamento de Terapia Intensiva Pediátrica, México, Distrito Federal. México |
Year: | 2010 |
Season: | Jul-Ago |
Volumen: | 31 |
Number: | 4 |
Pages: | 153-157 |
Country: | México |
Language: | Español |
Document type: | Artículo |
Approach: | Experimental, aplicado |
Spanish abstract | Los tumores cardiacos primarios son raros en la infancia y en su mayoría son benignos (97%). Los tumores primarios benignos más frecuentes son los rabdomiomas; 45% en autopsias y 79% series clínicas 1. En niños la incidencia es del 0.27% 2. Son benignos por sus características histológicas; sin embargo, pueden ser causa de diversas manifestaciones dependiendo del sitio en que se ubique el tumor, de las estructuras que involucren, obstruyan o dañen. La asociación con esclerosis tuberosa se ha observado hasta en un 81% de los pacientes. Se presenta el caso de un neonato, con rabdomioma cardiaco diagnosticado al nacimiento que causó bradicardia en la etapa fetal e insuficiencia cardiaca secundaria, presentando involución. Al año de vida el paciente está asintomático |
English abstract | Primary cardiac tumors are rare in childhood and are mostly benign (97%). Rhabdomyomas are the most frequent benign primary tumors with an incidence of 45% in autopsy series and 19% clinical series. In the pediatric population it incidence is 0.27%. They are benign tumors in view of their histological features. However, they may give rise to clinical manifestations depending on their location and on the structures they involve, obstruct or invade. They are associated with tuberous sclerosis has been observed up to 81% of the patients. We report a case of a newborn male who presented at birth with congestive heart failure (CHF), bradycardia. He was diagnosed as tuberous sclerosis with intracardiac rhabdomyoma which resolved spontaneously. Patient is currently asymptomatic one year after the initial diagnosis |
Disciplines: | Medicina |
Keyword: | Pediatría, Sistema cardiovascular, Tumores cardiacos, Rabdomioma, Esclerosis tuberosa, Bradicardia |
Keyword: | Medicine, Cardiovascular system, Pediatrics, Cardiac tumors, Rhabdomyoma, Tuberous sclerosis, Bradycardia |
Full text: | Texto completo (Ver PDF) |