Do you know this syndrome? Type 2 benign symmetric lipomatosis (Launois-Bensaude)



Document title: Do you know this syndrome? Type 2 benign symmetric lipomatosis (Launois-Bensaude)
Journal: Anais brasileiros de dermatologia
Database: PERIÓDICA
System number: 000404140
ISSN: 0365-0596
Authors: 1
1
1
1
Institutions: 1Universidade Estadual Paulista "Julio de Mesquita Filho", Faculdade de Medicina de Botucatu, Botucatu, Sao Paulo. Brasil
Year:
Season: Nov-Dic
Volumen: 91
Number: 6
Pages: 840-841
Country: Brasil
Language: Inglés
Document type: Artículo
Approach: Caso clínico
English abstract A 57-year-old female showed bulky, loose tumors, which progressively spread to her arms, anterior chest, and back. She reported dysphagia and dyspnea after mild exertion. She denied alcohol consumption. CT scan of her chest showed no internal lesions. Benign symmetric lipomatosis is a rare syndrome, clinically described as multiple nonencapsulated lipomas of various sizes and symmetrical distribution. This syndrome has three known phenotypes; in type 2 (Launois-Bensaude syndrome), lesions occur primarily on the shoulders, upper arms, and chest, and is unrelated to alcoholism. It causes aesthetic deformities and might block the upper airways. Mediastinal invasion might occur as well
Disciplines: Medicina
Keyword: Dermatología,
Lipomatosis simétrica,
Síndrome de Launois-Bensaude
Keyword: Medicine,
Dermatology,
Symmetric lipomatosis,
Launois-Bensaude syndrome
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