Do you know this syndrome? Type 2 benign symmetric lipomatosis (Launois-Bensaude)



Título del documento: Do you know this syndrome? Type 2 benign symmetric lipomatosis (Launois-Bensaude)
Revista: Anais brasileiros de dermatologia
Base de datos: PERIÓDICA
Número de sistema: 000404140
ISSN: 0365-0596
Autors: 1
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Institucions: 1Universidade Estadual Paulista "Julio de Mesquita Filho", Faculdade de Medicina de Botucatu, Botucatu, Sao Paulo. Brasil
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Període: Nov-Dic
Volum: 91
Número: 6
Paginació: 840-841
País: Brasil
Idioma: Inglés
Tipo de documento: Artículo
Enfoque: Caso clínico
Resumen en inglés A 57-year-old female showed bulky, loose tumors, which progressively spread to her arms, anterior chest, and back. She reported dysphagia and dyspnea after mild exertion. She denied alcohol consumption. CT scan of her chest showed no internal lesions. Benign symmetric lipomatosis is a rare syndrome, clinically described as multiple nonencapsulated lipomas of various sizes and symmetrical distribution. This syndrome has three known phenotypes; in type 2 (Launois-Bensaude syndrome), lesions occur primarily on the shoulders, upper arms, and chest, and is unrelated to alcoholism. It causes aesthetic deformities and might block the upper airways. Mediastinal invasion might occur as well
Disciplines Medicina
Paraules clau: Dermatología,
Lipomatosis simétrica,
Síndrome de Launois-Bensaude
Keyword: Medicine,
Dermatology,
Symmetric lipomatosis,
Launois-Bensaude syndrome
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