Revista: | Anais brasileiros de dermatologia |
Base de datos: | PERIÓDICA |
Número de sistema: | 000425690 |
ISSN: | 0365-0596 |
Autores: | Merlotto, Maira Renata1 Cantadori, Lucas Oliveira1 Sakabe, Delmo2 Miot, Helio Amante1 |
Instituciones: | 1Universidade Estadual Paulista "Julio de Mesquita Filho", Faculdade de Medicina de Botucatu, Botucatu, Sao Paulo. Brasil 2Pontificia Universidade Catolica de Sao Paulo, Departamento de Cirurgia, Sao Paulo. Brasil |
Año: | 2018 |
Periodo: | May-Jun |
Volumen: | 93 |
Número: | 3 |
Paginación: | 451-453 |
País: | Brasil |
Idioma: | Inglés |
Tipo de documento: | Artículo |
Enfoque: | Caso clínico, analítico |
Resumen en inglés | Hypereosinophilic syndrome is defined as persistent eosinophilia (>1500/µL for more than six months) associated with organ involvement, excluding secondary causes. It is a rare, potentially lethal disease that should be considered in cutaneous conditions associated with hypereosinophilia. We report a case of erythroderma as a manifestation of hypereosinophilic syndrome. A 36-year-old male with no comorbidities presented progressive erythroderma, pruritus, peripheral neuropathy, and eosinophilia in the previous seven months. No mutations were found in FIP1L1/PDGFRA. Patient experienced rapid remission in response to oral prednisone and hydroxyurea. Cutaneous manifestations may be the only evidence of hypereosinophilic syndrome. Genotyping excludes myeloproliferative disease, thereby orienting treatment and prognosis |
Disciplinas: | Medicina |
Palabras clave: | Dermatología, Diagnóstico diferencial, Eritrodermia, Eosinofilia, Síndrome hipereosinofílico, Dermatitis exfoliativa, Polineuropatías |
Keyword: | Dermatology, Differential diagnosis, Erythrodermia, Eosinophilia, Hypereosinophilic syndrome, Exfoliative dermatitis, Polyneuropathies |
Texto completo: | Texto completo (Ver HTML) |