Florid cemento-osseous dysplasia and peripheral giant cell granuloma in a patient with neurofibromatosis 1



Título del documento: Florid cemento-osseous dysplasia and peripheral giant cell granuloma in a patient with neurofibromatosis 1
Revista: Anais brasileiros de dermatologia
Base de datos: PERIÓDICA
Número de sistema: 000408877
ISSN: 0365-0596
Autores: 1
2
3
4
5
Instituciones: 1Universidade de Sao Paulo, Faculdade de Medicina, Sao Paulo. Brasil
2Universidade Estadual da Paraiba, Departamento de Odontologia, Araruna, Paraiba. Brasil
3Universidade Federal de Campina Grande, Departamento de Odontologia, Patos, Paraiba. Brasil
4Universidade de Pernambuco, Departamento de Odontologia, Recife, Pernambuco. Brasil
5Universidade Federal do Rio Grande do Norte, Departamento de Patologia Oral, Natal, Rio Grande do Norte. Brasil
Año:
Periodo: Mar-Abr
Volumen: 92
Número: 2
Paginación: 252-255
País: Brasil
Idioma: Inglés
Tipo de documento: Artículo
Enfoque: Caso clínico, descriptivo
Resumen en inglés We report a 35-year-old mulatto female patient with neurofibromatosis Type 1 who presented with facial asymmetry. The patient had two lesions: florid cemento-osseous dysplasia associated with peripheral giant cell granuloma. She was referred for surgical treatment of the peripheral giant cell granuloma and the florid cemento-osseous dysplasia was treated conservatively by a multidisciplinary team. So far, no changes have been observed in the patient's clinical status. We observed no recurrence of peripheral giant cell granuloma. To the best of our knowledge, the present case is the first report of a patient with neurofibromatosis Type 1 associated with a giant cell lesion and florid cemento-osseous dysplasia
Disciplinas: Medicina
Palabras clave: Dermatología,
Neurología,
Neurofibromatosis tipo 1,
Granuloma periférico de células gigantes,
Displasia ósea
Keyword: Medicine,
Dermatology,
Neurology,
Neurofibromatosis type 1,
Peripheral giant cell granuloma,
Bone dysplasia
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