Extrinsic compression of left main coronary artery from aneurysmal dilation of pulmonary trunk in a adolescent: involution after surgery occlusion of sinus venosus atrial septal defect and pulmonary trunk plasty for reduction



Document title: Extrinsic compression of left main coronary artery from aneurysmal dilation of pulmonary trunk in a adolescent: involution after surgery occlusion of sinus venosus atrial septal defect and pulmonary trunk plasty for reduction
Journal: Arquivos brasileiros de cardiologia
Database: PERIÓDICA
System number: 000289143
ISSN: 0066-782X
Authors: 1
1
1
1
1
1
1
1
Institutions: 1Universidade de Sao Paulo, Faculdade de Medicina de Ribeirao Preto, Ribeirao Preto, Sao Paulo. Brasil
Year:
Season: Feb
Volumen: 88
Number: 2
Pages: 40-43
Country: Brasil
Language: Portugués, inglés
Document type: Artículo
Approach: Caso clínico
English abstract We report the case of an adolescent referred with initial diagnosis of pulmonary hypertension. Non-invasive investigation disclosed a sinus venous atrial septal defect with pulmonary hypertension. The hemodynamic study confirmed diagnosis, and also showed extrinsic compression of left main coronary artery by pulmonary trunk. Surgical closure of the defect in addition to pulmonary trunk plasty were undertaken. Two years after the surgery the patient is well, with clinical signs of mild pulmonary hypertension, and showing no evidence - also on echocardiogram - of left coronary artery trunk obstruction
Portuguese abstract Relatamos o caso de um adolescente encaminhado com o diagnóstico de hipertensão pulmonar. A investigação não invasiva detectou comunicação interatrial seio venoso com sinais de hipertensão pulmonar. No estudo hemodinâmico o diagnóstico foi confirmado, sendo também notada compressão esquerda pelo tronco pulmonar. O paciente foi submetido à oclusão cirúrgica da comunicação interatrial e à plastia redutora do tronco pulmonar. Dois anos após o procedimento, o paciente encontra-se bem, com sinais clínicos e ecocardiográficos de hipertensão pulmonar discreta e sem evidências, também pelo ecocardiograma, de obstrução do tronco da artéria coronária esquerda
Disciplines: Medicina
Keyword: Cirugía,
Diagnóstico,
Sistema cardiovascular,
Hipertensión pulmonar,
Anomalías,
Coronarias,
Comunicación interventricular
Keyword: Medicine,
Cardiovascular system,
Diagnosis,
Surgery,
Pulmonary hypertension,
Coronary arteries,
Anomalies,
Atrial septal defect
Full text: Texto completo (Ver HTML)