Case for diagnosis. Lichen myxedematosus



Document title: Case for diagnosis. Lichen myxedematosus
Journal: Anais brasileiros de dermatologia
Database: PERIÓDICA
System number: 000404141
ISSN: 0365-0596
Authors: 1
2
3
1
Institutions: 1Faculdade Evangelica do Parana, Hospital Universitario Evangelico de Curitiba, Curitiba, Parana. Brasil
2Universidade Positivo, Curitiba, Parana. Brasil
3Universidade Federal do Parana, Curitiba, Parana. Brasil
Year:
Season: Nov-Dic
Volumen: 91
Number: 6
Pages: 842-845
Country: Brasil
Language: Inglés
Document type: Artículo
Approach: Caso clínico
English abstract Scleromyxedema or lichen myxedematosus is a rare papular mucinosis of chronic and progressive course and unknown etiology. It is commonly associated with monoclonal gammopathy and may show extracutaneous manifestations, affecting the heart, lung, kidney, and nerves. The diagnosis is based on four criteria: generalized papular and sclerodermoid lesions; mucin deposition, fibroblast proliferation, and fibrosis in the histopathology; monoclonal gammopathy; and no thyroid disorders. This article reports the case of a scleromyxedema patient with a recent history of acute myocardial infarction and monoclonal gammopathy
Disciplines: Medicina
Keyword: Dermatología,
Inmunología,
Escleromixedema,
Gamapatías monoclonales,
Mucinosis,
Paraproteinemia
Keyword: Medicine,
Dermatology,
Immunology,
Scleromyxedema,
Monoclonal gammopathies,
Mucinosis,
Paraproteinemia
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