Journal: | Anais brasileiros de dermatologia |
Database: | PERIÓDICA |
System number: | 000404141 |
ISSN: | 0365-0596 |
Authors: | Rebellato, Priscila Regina Orso1 Carbonar, Mauren Beatriz Frazon2 Tabuti, Nicole Iasmin Magario3 Rastelli, Graziela Junges Crescente1 |
Institutions: | 1Faculdade Evangelica do Parana, Hospital Universitario Evangelico de Curitiba, Curitiba, Parana. Brasil 2Universidade Positivo, Curitiba, Parana. Brasil 3Universidade Federal do Parana, Curitiba, Parana. Brasil |
Year: | 2016 |
Season: | Nov-Dic |
Volumen: | 91 |
Number: | 6 |
Pages: | 842-845 |
Country: | Brasil |
Language: | Inglés |
Document type: | Artículo |
Approach: | Caso clínico |
English abstract | Scleromyxedema or lichen myxedematosus is a rare papular mucinosis of chronic and progressive course and unknown etiology. It is commonly associated with monoclonal gammopathy and may show extracutaneous manifestations, affecting the heart, lung, kidney, and nerves. The diagnosis is based on four criteria: generalized papular and sclerodermoid lesions; mucin deposition, fibroblast proliferation, and fibrosis in the histopathology; monoclonal gammopathy; and no thyroid disorders. This article reports the case of a scleromyxedema patient with a recent history of acute myocardial infarction and monoclonal gammopathy |
Disciplines: | Medicina |
Keyword: | Dermatología, Inmunología, Escleromixedema, Gamapatías monoclonales, Mucinosis, Paraproteinemia |
Keyword: | Medicine, Dermatology, Immunology, Scleromyxedema, Monoclonal gammopathies, Mucinosis, Paraproteinemia |
Full text: | Texto completo (Ver HTML) |